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ACTIVE NOT RECRUITING
NCT05445323
PHASE1/PHASE2

Gene Therapy for Cardiomyopathy Associated With Friedreich's Ataxia

Sponsor: Lexeo Therapeutics

View on ClinicalTrials.gov

Summary

This is a Phase 1/2, open-label, dose-ascending, multicenter study of the safety and efficacy of LX2006 for participants who have Friedreich's Ataxia with evidence of cardiomyopathy. The study will evaluate up to three doses of single administration of LX2006 (AAVrh.10hFXN), an adeno-associated virus (AAV) gene therapy designed to intravenously deliver the human frataxin (hFXN) gene to cardiac cells over a 52-week period. Long-term safety and efficacy will be evaluated for an additional 4-years for a total of 5-years post LX2006 treatment.

Official title: A Phase 1/2 Study of the Safety and Efficacy of LX2006 Gene Therapy in Participants With Cardiomyopathy Associated With Friedreich's Ataxia

Key Details

Gender

All

Age Range

18 Years - 50 Years

Study Type

INTERVENTIONAL

Enrollment

8

Start Date

2022-08-24

Completion Date

2029-09

Last Updated

2025-12-23

Healthy Volunteers

No

Interventions

GENETIC

Low dose LX2006

Adeno-associated viral vector encoding the FXN gene (AAVrh.10hFXN)

GENETIC

Mid Dose LX2006

Adeno-associated viral vector encoding the FXN gene (AAVrh.10hFXN)

GENETIC

High Dose LX2006

Adeno-associated viral vector encoding the FXN gene (AAVrh.10hFXN)

Locations (3)

Ataxia Center and HD Center of Excellence, University of California

Los Angeles, California, United States

University of South Florida

Tampa, Florida, United States

Mayo Clinic

Rochester, Minnesota, United States