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Dietary Treatment Strategies and Metabolic Control in Glycogen Storage Disease Type I
Sponsor: Insel Gruppe AG, University Hospital Bern
Summary
The present project will specifically assess metabolic effects of dietary interventions with controlled intake of fructose and fructose/galactose in GSDI, with the aim to provide evidence whether relaxed dietary restrictions of fructose and galactose may be justified in treatment recommendations at least for adults, which would considerably enlarge food choice in everyday life of the patients with an expected positive impact on the quality of life of patients with this rare disorder.
Official title: Dietary Treatment Strategies and Metabolic Control in Glycogen Storage Disease Type I (GSD-DIET)
Key Details
Gender
All
Age Range
18 Years - Any
Study Type
INTERVENTIONAL
Enrollment
20
Start Date
2025-04-24
Completion Date
2027-03
Last Updated
2025-04-24
Healthy Volunteers
No
Conditions
Interventions
Fructose
40g fructose (free and bound, max amount of fructose from added free sugar/saccharose 25g)
Fructose and galactose
10g galactose (mostly from lactose) plus 40g of fructose (free and bound, max amount of fructose from added free sugar/saccharose 25g)
Locations (1)
Department of Diabetes, Endocrinology, Nutritional Medicine and Metabolism, Inselspital, Bern University Hospital
Bern, Switzerland