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RECRUITING
NCT06941389

Comparing the Effectiveness of Matched Related Donor Hematopoietic Stem Cell Transplantation to Disease Modifying Therapy in Pediatric Patients With Sickle Cell Disease

Sponsor: University of Rochester

View on ClinicalTrials.gov

Summary

The WeDecide study is a large observational study comparing the long-term effects of matched related donor hematopoietic stem cell transplantation (MRD HCT) and non-transplant disease-modifying therapies (NT-DMT) for pediatric patients with sickle cell disease (SCD). The study aims to assess health-related quality of life (HRQoL), cognitive function, risks, and benefits of both treatments, including survival rates, chronic complications, and organ damage prevention. With 160 children in the MRD HCT group and 320 in the NT-DMT group, aged 3-20.9 years, the study will follow participants for three years, examining factors like disease severity, treatment history, and social determinants of health. By providing a comprehensive comparison, the study seeks to inform clinical decisions and improve understanding of SCD treatment outcomes, ultimately supporting families and healthcare providers in choosing the best treatment options.

Official title: Comparing the Effectiveness of Matched Related Donor Hematopoietic Stem Cell Transplantation to Disease Modifying Therapy in Pediatric Patients With Sickle Cell Disease.

Key Details

Gender

All

Age Range

3 Years - 20 Years

Study Type

OBSERVATIONAL

Enrollment

480

Start Date

2024-06-01

Completion Date

2030-10-01

Last Updated

2025-06-19

Healthy Volunteers

No

Locations (37)

Children's of Alabama (MRD-HCT)

Birmingham, Alabama, United States

Children's of Alabama (NT-DMT)

Birmingham, Alabama, United States

Nemours Children's Hospital, Delaware (MRD-HCT)

Wilmington, Delaware, United States

Children's National Hospital (MRD-HCT)

Washington D.C., District of Columbia, United States

Children's Healthcare of Atlanta (MRD-HCT)

Atlanta, Georgia, United States

Comer Children's Hospital (MRD-HCT)

Chicago, Illinois, United States

Riley Children's Hospital (MRD-HCT)

Indianapolis, Indiana, United States

Riley's Children Hospital (NT-DMT)

Indianapolis, Indiana, United States

Boston Children's Hospital (MRD-HCT)

Boston, Massachusetts, United States

Boston Children's Hospital (NT-DMT)

Boston, Massachusetts, United States

Wahington Univ in St Louis (NT-DMT)

St Louis, Missouri, United States

Washington University in St Louis (MRD-HCT)

St Louis, Missouri, United States

Hackensack University Hospital (MRD-HCT)

Hackensack, New Jersey, United States

Roswell Park (MRD-HCT)

Buffalo, New York, United States

Columbia Presbytarian (NT-DMT)

New York, New York, United States

Cohen's Children Hospital (NT-DMT)

Queens, New York, United States

University of Rochester (MRD-HCT)

Rochester, New York, United States

University of Rochester (NT-DMT)

Rochester, New York, United States

Children's Hospital at Montefiore (MRD HCT)

The Bronx, New York, United States

Children's Hospital at Montefiore (NT-DMT)

The Bronx, New York, United States

UNC Children's Hospital (MRD HCT)

Chapel Hill, North Carolina, United States

UNC Children's Hospital (NT-DMT)

Chapel Hill, North Carolina, United States

Atrium Health (MRD-HCT)

Charlotte, North Carolina, United States

Nationwide Children's Hospital (NT-DMT)

Columbus, Ohio, United States

Oklahoma Children's Hospital (MRD-HCT)

Oklahoma City, Oklahoma, United States

Children's Hospital of Philadelphia (MRD-HCT)

Philadelphia, Pennsylvania, United States

St Jude Children Hospital (NT-DMT)

Memphis, Tennessee, United States

St. Jude Children's Research Hospital (MRD-HCT)

Memphis, Tennessee, United States

Texas Children's Hopsital (NT-DMT)

Houston, Texas, United States

Texas Children's Hospital (MRD-HCT)

Houston, Texas, United States

UT San Antonio (NT-DMT)

San Antonio, Texas, United States

Alberta Children's Hospital (NT-DMT)

Calgary, Alberta, Canada

Alberta Children's Hospital (MRD-HCT)

Calgary, Alberta, Canada

British Columbia Children's Hosptial (MRD HCT)

Vancouver, British Columbia, Canada

HSC Winnipeg Children's Hospital/University of Manitoba (MRD-HCT)

Winnipeg, Manitoba, Canada

The Hospital for Sick Children (MRD-HCT)

Toronto, Ontario, Canada

Universite de Montreal / Ste Justine (MRD HCT)

Montreal, Quebec, Canada